Gorlin-Goltz-Syndrom

Masses of

developmental and genetic origin affecting the paediatric craniofacial skeleton. Typical manifestations of nevoid basal cell carcinoma syndrome (NBCCS) in a 16-year-old boy. a Orthopantomography (OPT) shows cystic lesions of the mandible and maxilla (arrows), with unilocular and multilocular pattern and smooth or scalloped borders associated with displaced and unerupted permanent teeth. b Coronal CT scan (bone window) shows ectopic calcifications of the falx cerebri and tentorium cerebelli (arrows) and spotted meningeal calcifications (arrowheads). Brain MRI reveals a cavum veli interpositi on axial T2 (asterisk in c) and coronal contrast-enhanced T1 (asterisk in d) and also vermian dysgenesis (arrowheads in d)

Gorlin-Goltz

syndrome • Gorlin-Goltz syndrome - Ganzer Fall bei Radiopaedia

Gorlin-Goltz

syndrome • Gorlin syndrome - Ganzer Fall bei Radiopaedia

Gorlin-Goltz

syndrome • Gorlin-Goltz syndrome - Ganzer Fall bei Radiopaedia

Gorlin-Goltz

syndrome • Gorlin-Goltz syndrome - incidental posterior communicating aneurysm - Ganzer Fall bei Radiopaedia

Gorlin-Goltz

syndrome • Odontogenic keratocysts - Ganzer Fall bei Radiopaedia

Gorlin-Goltz

syndrome • Gorlin-Goltz syndrome - Ganzer Fall bei Radiopaedia

School ager

with a bump on the right side of the face. Axial (above), coronal (below left) and sagittal (below right) CT without contrast of the face shows a lytic, expansile lesion in the right maxilla displacing the second right premolar tooth anterolateraly. There was no bone destruction or associated soft tissue mass.The diagnosis was an odontogenic keratocyst in a patient with Gorlin syndrome.